Iyo protagonist yemusangano uyu unonakidza unonzi Sam Berns. Nehurombo akatofa (ingangoita mwedzi mitatu abata musangano uyu).
Mariri zvinotiratidza uzivi hwake hwehupenyu iyo yakavakirwa pamapoinzi matatu. Izvo zvakakodzera kuteerera uyu mukomana uyo hupenyu hwave husina kuve nyore uye izvo zvisina kumutadzisa kuti afare kusvika pazuva rekupedzisira rehupenyu hwake.
Anotaura nezvekuti usatarise pane zvaunogumira, izvo zvausingakwanise kana kushandura, uye tarisa pane zvatingaite uye tinofarira:
Kana iwe waifarira vhidhiyo iyi, iigovana neshamwari dzako!
[social4i size = »hombe» enzanisa = »tarisa-kuruboshwe»]
Vabereki vaSam, Dr. Leslie Gordon naScott Berns, yakavambwa Iyo Progeria Ongororo Foundation (iyo Progeria Research Foundation) muna 1999 kutsvaga chikonzero, kurapwa uye kurapwa kwechirwere chisingawanzoitika. Vana vane Progeria vanorarama avhareji yemakore gumi nematatu.
Mu progeria, kukwegura zviratidzo zvinogona kuoneka kubva mugore rekutanga rehupenyu.
Vana, kana vaine makore mashanu kana masere ekuberekwa, vanorasikirwa nevhudzi ravo, ganda ravo rinounyana, vanotambura neatherosclerosis, osteoporosis kana arthritis, zvirwere zvevakwegura.
Kune munhu mumwe chete akararama kusvika pamakore makumi maviri nematanhatu ekuberekwa. Aive mukomana anonzi Leon Botha anobva kuSouth Africa. Akafa muna 26 kubva kumatambudziko eProgeria.
Pane zvinowirirana zvinowirirana pakati pevana vane Progeria uye nehuwandu hwevanhu vakwegura. Isu tese tinoita imwe progerin, iyo-inokonzera chirwere protein muProgeria. Vana vane Progeria vanoita zvakanyanya progerin.